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Vivien Béziat

@vbeziat.bsky.social

INSERM researcher at Imagine Institute Study Inborn Errors of immunity

Vivien Béziat @vbeziat.bsky.social · 09/01/2026

🧬 New in @cellpress.bsky.social 🧵 1/ With @casanovalab.bsky.social , we propose a rethinking of monogenic disorders of immunity: 👉 common variants can matter — a lot.

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Vivien Béziat @vbeziat.bsky.social · 06/06/2025

🚨 Our first paper in @jhumimmunity.org just came out! We describe two forms of TCR⍺ deficiency: a complete and a partial form. 👉 doi.org/10.70962/jhi...

doi.org

Two different forms of inherited human TCRα chain deficiency | Journal of Human Immunity | Rockefeller University Press

Previous reports suggested that inherited TCRα deficiency is not as severe as expected. We report children with complete TCRα deficiency, a lack of αβ T ce

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Reposted by Vivien Béziat

Journal of Human Immunity @jhumimmunity.org · 04/06/2025

Materna, @vbeziat.bsky.social‬ et al. @institutimagine.bsky.social‬ report children with complete TCRα deficiency, a lack of αβ T cells, & a severe condition. Previously characterized TCRα deficiency, which wasn't as severe as expected, was partial, as opposed to complete rupress.org/jhi/article/...

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Reposted by Vivien Béziat

Rockefeller University Press @rupress.org · 04/06/2025

New in @jhumimmunity.org: Materna, @vbeziat.bsky.social‬ et al. report children with complete TCRα deficiency, a lack of αβ T cells, & a severe condition. Previously characterized TCRα deficiency, which wasn't as severe as expected, was partial, as opposed to complete rupress.org/jhi/article/...

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